Budd-Chiari Syndrome

Common Name(s)

Budd-Chiari Syndrome

Budd-Chiari syndrome is a rare disorder characterized by narrowing and obstruction of the veins of the liver. This narrowing or obstruction slows or prevents blood from flowing out of the liver and back to the heart which can lead to liver damage. While some people experience no symptoms, many experience fatigue, abdominal pain, nausea, and jaundice. Other associated findings include an accumulation of fluid in the abdomen (ascites), an enlarged spleen and/or liver, and severe bleeding in the esophagus. The severity of the disorder varies from case to case, depending on the site and number of affected veins. Drugs may be used to dissolve or decrease the size of the obstruction (if it is a clot). In some cases surgery is performed.  In most cases, the cause of Budd-Chiari syndrome is unknown.
 

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Budd-Chiari Syndrome" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Budd-Chiari Syndrome" returned 215 free, full-text research articles on human participants. First 3 results:

Myeloproliferative neoplasms and recurrent thrombotic events in patients undergoing liver transplantation for Budd-Chiari syndrome: a single-center experience.
 

Author(s): Urszula Oldakowska-Jedynak, Mateusz Ziarkiewicz, Bogna Ziarkiewicz-Wróblewska, Jadwiga Dwilewicz-Trojaczek, Barbara Górnicka, Paweł Nyckowski, Rafał Paluszkiewicz, Tadeusz Wróblewski, Krzysztof Zieniewicz, Waldemar Patkowski, Leszek Pączek, Wiesław Wiktor Jedrzejczak, Marek Krawczyk

Journal:

 

Budd-Chiari syndrome is a heterogeneous disease. The role of liver transplantation as a treatment option has been discussed since 1976. Many cases are related to underlying myeloproliferative neoplasms associated with prothrombotic propensity. The aim of this study was to evaluate ...

Last Updated: 14 Nov 2014

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Correction of the Scimitar syndrome, a rare cardiac venous anomaly, leading to Budd-Chiari syndrome: a case report.
 

Author(s): Marie-Pia Assoignon, Paul Christiaens, Wim Laleman

Journal:

 

Scimitar syndrome is a congenital heart disease characterized by an abnormal drainage of the right lung into the inferior vena cava, the right atrium or a variety of venous connections from the anomalous pulmonary vein to a systemic vein. This left-to-right shunt induces pulmonary ...

Last Updated: 20 Aug 2014

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Images in clinical medicine. Abdominal-wall varices in the Budd-Chiari syndrome.
 

Author(s): Xingshun Qi, Guohong Han

Journal: N. Engl. J. Med.. 2014 May;370(19):1829.

 

Last Updated: 8 May 2014

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Budd-Chiari Syndrome" returned 14 free, full-text review articles on human participants. First 3 results:

An update on management of Budd-Chiari syndrome.
 

Author(s): Andrea Mancuso

Journal: Ann Hepatol. ;13(3):323-6.

 

The topic of this paper is to report an update on management of Budd-Chiari syndrome (BCS). Actually, the flow-chart of BCS management comes from experts opinion and is not evidence-based due to the rarity of BCS. Management of BCS follows a step-wise strategy. Anticoagulation and ...

Last Updated: 23 Apr 2014

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Scientific publications on portal vein thrombosis and Budd-Chiari syndrome: a global survey of the literature.
 

Author(s): Xingshun Qi, Jia Jia, Weirong Ren, Man Yang, Valerio De Stefano, Juan Wang, Daiming Fan

Journal: J Gastrointestin Liver Dis. 2014 Mar;23(1):65-71.

 

Portal vein thrombosis (PVT) and Budd-Chiari syndrome (BCS) are two rare vascular disorders of the liver that can lead to life-threatening complications. We conducted a global survey to systematically analyze the scientific publications in the fields of PVT and BCS.

Last Updated: 1 Apr 2014

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The Budd-Chiari syndrome.
 

Author(s): Rania Hefaiedh, Mariem Cheikh, Lobna Marsaoui, Rym Ennaifer, Hayfa Romdhane, Houda Ben Nejma, Najet Bel Hadj, Nafaa Arfa, Mohamed Taher Khalfallah

Journal: Tunis Med. 2013 Jun;91(6):376-81.

 

The Budd-Chiari syndrome is a rare disease, often fatal if not treated optimally. It is characterized by a blocked hepatic venous outflow tract. aim: This review attempted to present pathophysiology, aetiologies,diagnosis and therapeutic modalities of the Budd-Chiari syndrome.

Last Updated: 22 Jul 2013

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Symptoms, Diagnosis, and Treatment

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Clinical Trial Information This information is provided by ClinicalTrials.gov

Budd-Chiari Syndrome in China: Balloon Angioplasty Alone or Combined With Stent Placement?
 

Status: Recruiting

Condition Summary: Budd-Chiari Syndrome

 

Last Updated: 25 Jul 2014

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Defibrotide for Patients With Hepatic Veno-occlusive Disease: A Treatment IND Study
 

Status: Recruiting

Condition Summary: Hepatic Veno-Occlusive Disease

 

Last Updated: 19 Jun 2015

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Effects on Glutamine on the Outcome of Allogeneic Bone Marrow Transplant Recipients
 

Status: Recruiting

Condition Summary: Pulmonary Veno-Occlusive Disease; Hepatic Veno-Occlusive Disease; Mucositis

 

Last Updated: 6 Jul 2010

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