Budd-Chiari Syndrome

Common Name(s)

Budd-Chiari Syndrome

Budd-Chiari syndrome is a rare disorder characterized by narrowing and obstruction of the veins of the liver. This narrowing or obstruction slows or prevents blood from flowing out of the liver and back to the heart which can lead to liver damage. While some people experience no symptoms, many experience fatigue, abdominal pain, nausea, and jaundice. Other associated findings include an accumulation of fluid in the abdomen (ascites), an enlarged spleen and/or liver, and severe bleeding in the esophagus. The severity of the disorder varies from case to case, depending on the site and number of affected veins. Drugs may be used to dissolve or decrease the size of the obstruction (if it is a clot). In some cases surgery is performed.  In most cases, the cause of Budd-Chiari syndrome is unknown.
 

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How do you compare to others with this condition?

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Budd-Chiari Syndrome" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Budd-Chiari Syndrome" returned 256 free, full-text research articles on human participants. First 3 results:

Colon perforation and Budd-Chiari syndrome in Behçet's disease.
 

Author(s): Yılmaz Baş, Güven Güney, Pınar Uzbay, Ethem Zobacı, Selin Ardalı, Ayşegül Taylan Özkan

Journal:

 

Behçet's disease is a chronic inflammatory disease involving multiple systems, with vasculitis being the most important pathological feature. Multiple colon perforations are thought to be secondary to vasculitis and they occur in patients with ulcers. These may be encountered within ...

Last Updated: 2 May 2015

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Budd-Chiari syndrome with multiple large regenerative nodules.
 

Author(s): Haeryoung Kim, Ji Hae Nahm, Young Nyun Park

Journal: Clin Mol Hepatol. 2015 Mar;21(1):89-94.

 

Last Updated: 2 Apr 2015

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Portal vein aneurysm associated with Budd-Chiari syndrome treated with transjugular intrahepatic portosystemic shunt: a case report.
 

Author(s): Jiaywei Tsauo, Xiao Li

Journal: World J. Gastroenterol.. 2015 Mar;21(9):2858-61.

 

A 65-year-old woman with Budd-Chiari syndrome (BCS) presented with right upper quadrant pain. A computed tomography (CT) scan showed a saccular aneurysm located at the extrahepatic portal vein main branch measuring 3.2 cm in height and 2.5 cm × 2.4 cm in diameter. The aneurysm was ...

Last Updated: 11 Mar 2015

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Budd-Chiari Syndrome" returned 18 free, full-text review articles on human participants. First 3 results:

Selection of treatment modalities for Budd-Chiari Syndrome in China: a preliminary survey of published literature.
 

Author(s): Xing-Shun Qi, Wei-Rong Ren, Dai-Ming Fan, Guo-Hong Han

Journal: World J. Gastroenterol.. 2014 Aug;20(30):10628-36.

 

To evaluate the frequency of use of various treatment modalities for Budd-Chiari syndrome (BCS) in China by conducting a preliminary survey of relevant literature.

Last Updated: 18 Aug 2014

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An update on management of Budd-Chiari syndrome.
 

Author(s): Andrea Mancuso

Journal: Ann Hepatol. ;13(3):323-6.

 

The topic of this paper is to report an update on management of Budd-Chiari syndrome (BCS). Actually, the flow-chart of BCS management comes from experts opinion and is not evidence-based due to the rarity of BCS. Management of BCS follows a step-wise strategy. Anticoagulation and ...

Last Updated: 23 Apr 2014

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Scientific publications on portal vein thrombosis and Budd-Chiari syndrome: a global survey of the literature.
 

Author(s): Xingshun Qi, Jia Jia, Weirong Ren, Man Yang, Valerio De Stefano, Juan Wang, Daiming Fan

Journal: J Gastrointestin Liver Dis. 2014 Mar;23(1):65-71.

 

Portal vein thrombosis (PVT) and Budd-Chiari syndrome (BCS) are two rare vascular disorders of the liver that can lead to life-threatening complications. We conducted a global survey to systematically analyze the scientific publications in the fields of PVT and BCS.

Last Updated: 1 Apr 2014

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Symptoms, Diagnosis, and Treatment

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Clinical Trial Information This information is provided by ClinicalTrials.gov

Budd-Chiari Syndrome in China: Balloon Angioplasty Alone or Combined With Stent Placement?
 

Status: Recruiting

Condition Summary: Budd-Chiari Syndrome

 

Last Updated: 25 Jul 2014

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Defibrotide for Patients With Hepatic Veno-occlusive Disease: A Treatment IND Study
 

Status: Recruiting

Condition Summary: Hepatic Veno-Occlusive Disease

 

Last Updated: 5 Feb 2016

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Effects on Glutamine on the Outcome of Allogeneic Bone Marrow Transplant Recipients
 

Status: Recruiting

Condition Summary: Pulmonary Veno-Occlusive Disease; Hepatic Veno-Occlusive Disease; Mucositis

 

Last Updated: 6 Jul 2010

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