Auditory Neuropathy

Common Name(s)

Auditory Neuropathy

Description for this condition is not yet available.
 

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Auditory Neuropathy" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Auditory Neuropathy" returned 45 free, full-text research articles on human participants. First 3 results:

OPA1-related auditory neuropathy: site of lesion and outcome of cochlear implantation.
 

Author(s): Rosamaria Santarelli, Roberta Rossi, Pietro Scimemi, Elona Cama, Maria Lucia Valentino, Chiara La Morgia, Leonardo Caporali, Rocco Liguori, Vincenzo Magnavita, Anna Monteleone, Ariella Biscaro, Edoardo Arslan, Valerio Carelli

Journal: Brain. 2015 Mar;138(Pt 3):563-76.

 

Hearing impairment is the second most prevalent clinical feature after optic atrophy in dominant optic atrophy associated with mutations in the OPA1 gene. In this study we characterized the hearing dysfunction in OPA1-linked disorders and provided effective rehabilitative options ...

Last Updated: 25 Feb 2015

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Inter-trial coherence as a marker of cortical phase synchrony in children with sensorineural hearing loss and auditory neuropathy spectrum disorder fitted with hearing aids and cochlear implants.
 

Author(s): Amy Nash-Kille, Anu Sharma

Journal: Clin Neurophysiol. 2014 Jul;125(7):1459-70.

 

Although brainstem dys-synchrony is a hallmark of children with auditory neuropathy spectrum disorder (ANSD), little is known about how the lack of neural synchrony manifests at more central levels. We used time-frequency single-trial EEG analyses (i.e., inter-trial coherence; ITC), ...

Last Updated: 26 May 2014

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Impact of the presence of auditory neuropathy spectrum disorder (ANSD) on outcomes of children at three years of age.
 

Author(s): Teresa Y C Ching, Julia Day, Harvey Dillon, Kirsty Gardner-Berry, Sanna Hou, Mark Seeto, Angela Wong, Vicky Zhang

Journal: Int J Audiol. 2013 Dec;52 Suppl 2():S55-64.

 

To determine the influence of the presence of auditory neuropathy spectrum disorder (ANSD) on speech, language, and psycho-social development of children at three years of age.

Last Updated: 19 Dec 2013

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Auditory Neuropathy" returned 4 free, full-text review articles on human participants. First 3 results:

Plasticity in the developing auditory cortex: evidence from children with sensorineural hearing loss and auditory neuropathy spectrum disorder.
 

Author(s): Garrett Cardon, Julia Campbell, Anu Sharma

Journal: J Am Acad Audiol. 2012 Jun;23(6):396-411; quiz 495.

 

The developing auditory cortex is highly plastic. As such, the cortex is both primed to mature normally and at risk for reorganizing abnormally, depending upon numerous factors that determine central maturation. From a clinical perspective, at least two major components of development ...

Last Updated: 6 Jun 2012

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Synchronous auditory nerve activity in the carboplatin-chinchilla model of auditory neuropathy.
 

Author(s): C D Cowper-Smith, R N Dingle, Y Guo, R Burkard, D P Phillips

Journal: J. Acoust. Soc. Am.. 2010 Jul;128(1):EL56-62.

 

Two hallmark features of auditory neuropathy (AN) are normal outer hair cell function in the presence of an absent/abnormal auditory brainstem response (ABR). Studies of human AN patients are unable to determine whether disruption of the ABR is the result of a reduction of neural ...

Last Updated: 23 Jul 2010

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Extratympanic electrocochleography in the diagnosis of auditory neuropathy/auditory dyssynchrony.
 

Author(s): Adriana Ribeiro Tavares Anastasio, Kátia de Freitas Alvarenga, Orozimbo Alves Costa Filho

Journal: Braz J Otorhinolaryngol. ;74(1):132-6.

 

The brainstem auditory evoked potential (BAEP) is being extensively used as a method for the evaluation of cochlear function in individuals with diagnosis of auditory neuropathy/auditory dyssynchrony (AN/AD). In the absence of otoacoustic emissions, many cases of AN/AD have been diagnosed ...

Last Updated: 8 Apr 2008

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Symptoms, Diagnosis, and Treatment

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Clinical Trial Information This information is provided by ClinicalTrials.gov

Auditory Brainstem Implantation in Young Children
 

Status: Recruiting

Condition Summary: Developmental Cochlear Nerve Deficiency; Acquired Cochlear Nerve Deficiency; Cochlear Aplasia; Post-meningitis Cochlear Ossification; Cochlear Malformation

 

Last Updated: 5 Apr 2014

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