Retroperitoneal fibrosis

Common Name(s)

Retroperitoneal fibrosis, Ormond's Disease

Retroperitoneal fibrosis is a slowly progressive disorder in which the tubes that carry urine from the kidneys to the bladder (ureters) and other abdominal organs are blocked by a fibrous mass and inflammation in the back of the abdomen. The disorder may cause chronic unilateral obstructive uropathy or chronic bilateral obstructive uropathy. Risk factors for retroperitoneal fibrosis include asbestos exposure, smoking, tumor, infection, trauma, radiotherapy, surgery, and use of certain drugs.
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Retroperitoneal fibrosis" for support, advocacy or research.

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Retroperitoneal Fibrosis World Support

We offer both a warm and comforting welcome and an unrivaled learning experience to build self awareness of RF. We welcome all patients, caregivers, family, friends, and interested medical professionals. This forum is for each member to offer others moral support, friendship, and opinions and advice based on our personal experiences with RF This group includes access to unsurpassed resources of professional papers, case histories, files, relevant links, a member recommended doctor database, information tables, and much more; to allow meaningful, valued exchanges and social interaction.

Last Updated: 29 Mar 2015

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General Support Organizations

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How do you compare to others with this condition?

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Anonymously share and see how your answers compare with others with this condition while privately providing key pieces of information to medical researchers, disease advocacy groups, and others ONLY YOU select to help speed up cures and better alternatives.

 
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Retroperitoneal fibrosis" for support, advocacy or research.

Logo
Retroperitoneal Fibrosis World Support

We offer both a warm and comforting welcome and an unrivaled learning experience to build self awareness of RF. We welcome all patients, caregivers, family, friends, and interested medical professionals. This forum is for each member to offer others moral support, friendship, and opinions and advice based on our personal experiences with RF This group includes access to unsurpassed resources of professional papers, case histories, files, relevant links, a member recommended doctor database, information tables, and much more; to allow meaningful, valued exchanges and social interaction.

https://groups.yahoo.com/neo/groups/retroperitoneal_fibrosisworldsuppo ...

Last Updated: 29 Mar 2015

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Retroperitoneal fibrosis" returned 214 free, full-text research articles on human participants. First 3 results:

Differentiation of Lymphoma Presenting as Retroperitoneal Mass and Retroperitoneal Fibrosis: Evaluation with Multidetector-row Computed Tomography.
 

Author(s): Shuai Zhang, Min Chen, Chun-Mei Li, Guo-Dong Song, Ying Liu

Journal: Chin. Med. J.. 2017 Mar;130(6):691-697.

 

Retroperitoneal fibrosis (RPF) and lymphoma presenting as retroperitoneal mass may closely resemble each other and misdiagnosis may occur. This study investigated the differential imaging features of RPF and lymphoma which presented as a retroperitoneal soft tissue using multidetector-row ...

Last Updated: 17 Mar 2017

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Idiopathic retroperitoneal fibrosis causing unilateral ureteral and sigmoid colon obstruction: A case report.
 

Author(s): Ting Yan, Yujuan Wang, Zhijun Liu, Xiaolei Zhang, Qian Wu, Mingrong Xi

Journal: Medicine (Baltimore). 2017 Feb;96(7):e6105.

 

The present report aimed to present a unique case of idiopathic retroperitoneal fibrosis (RPF) presenting features of unilateral ureteral and sigmoid colon obstruction. RPF is a rare disorder with unclear etiology.

Last Updated: 16 Feb 2017

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IgG4-related retroperitoneal fibrosis: A case report and review of literature.
 

Author(s): Azra Niaz, Asad Hayat Ahmad, , Muhammed Ahmad Saeed, Omer Sabir, Nauman Tarif

Journal: J Pak Med Assoc. 2016 Feb;66(2):220-2.

 

Idiopathic Retroperitoneal fibrosis is a rare clinical condition recently identified as an autoimmune process related to Immunoglobulin G4 (IgG4) deposition. Herein we report a case of a 46 year old male presenting with 4 months history of backache, fever, flank pain and leg swelling ...

Last Updated: 28 Jan 2016

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Retroperitoneal fibrosis" returned 20 free, full-text review articles on human participants. First 3 results:

Overlap of Post-obstructive Diuresis and Unmasked Diabetes Insipidus in a Case of IgG4-related Retroperitoneal Fibrosis and Tuberoinfundibular Hypophysitis: A Case Report and Review of the Literature.
 

Author(s): Midori Sasaki Yatabe, Kimio Watanabe, Yoshimitsu Hayashi, Junichi Yatabe, Satoshi Morimoto, Atsuhiro Ichihara, Masaaki Nakayama, Tsuyoshi Watanabe

Journal: Intern. Med.. ;56(1):47-53.

 

The clinical picture of IgG4-related disease (IgG4-RD) is diverse because various organs can be affected. We describe the case of a 56-year-old man with acute renal failure and tuberoinfundibular hypophysitis due to IgG4-RD. Steroid therapy lowered the serum IgG4 level and ameliorated ...

Last Updated: 4 Jan 2017

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Idiopathic Retroperitoneal Fibrosis.
 

Author(s): Augusto Vaglio, Federica Maritati

Journal: J. Am. Soc. Nephrol.. 2016 Jul;27(7):1880-9.

 

Idiopathic retroperitoneal fibrosis (RPF), reviewed herein, is a rare fibro-inflammatory disease that develops around the abdominal aorta and the iliac arteries, and spreads into the adjacent retroperitoneum, where it frequently causes ureteral obstruction and renal failure. The clinical ...

Last Updated: 1 Jul 2016

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[Clinical characteristics of IgG4 related retroperitoneal fibrosis: a report of 5 cases and literature review].
 

Author(s): Yao-jun Dun, Lu-ping Yu, Yi-qing Du, Zheng-zuo Sheng, Gong-wei Wang, Xue Li, Bing Yang, Tao Xu, Xiao-bo Huang, Xiao-feng Wang

Journal: Beijing Da Xue Xue Bao. 2015 Aug;47(4):622-7.

 

To explore the clinical characteristics, treatment and prognosis of IgG4-related retroperitoneal fibrosis (RPF).

Last Updated: 19 Aug 2015

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Clinical Trial Information This information is provided by ClinicalTrials.gov

Aortitis and Retroperitoneal Fibrosis: Evaluation of Diagnostic Criteria
 

Status: Recruiting

Condition Summary: Idiopathic Aortitis; Retroperitoneal Fibrosis

 

Last Updated: 25 Apr 2017

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Treatment of IgG4-Related Disease With Revlimid and Rituximab
 

Status: Recruiting

Condition Summary: Immunoglobulin G Subclass 4 Related Disease; IgG4-related Disease; Autoimmune Pancreatitis; IgG4-related Sclerosing Cholangitis; Retroperitoneal Fibrosis

 

Last Updated: 12 Sep 2016

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Leflunomide for Maintenance of Remission in IgG4 Related Disease
 

Status: Recruiting

Condition Summary: Immunoglobulin G4 Related Sclerosing Disease

 

Last Updated: 30 Mar 2016

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