Retroperitoneal fibrosis

Common Name(s)

Retroperitoneal fibrosis, Ormond's Disease

Retroperitoneal fibrosis is a slowly progressive disorder in which the tubes that carry urine from the kidneys to the bladder (ureters) and other abdominal organs are blocked by a fibrous mass and inflammation in the back of the abdomen. The disorder may cause chronic unilateral obstructive uropathy or chronic bilateral obstructive uropathy. Risk factors for retroperitoneal fibrosis include asbestos exposure, smoking, tumor, infection, trauma, radiotherapy, surgery, and use of certain drugs.
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Retroperitoneal fibrosis" for support, advocacy or research.

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Retroperitoneal Fibrosis World Support

We offer both a warm and comforting welcome and an unrivaled learning experience to build self awareness of RF. We welcome all patients, caregivers, family, friends, and interested medical professionals. This forum is for each member to offer others moral support, friendship, and opinions and advice based on our personal experiences with RF This group includes access to unsurpassed resources of professional papers, case histories, files, relevant links, a member recommended doctor database, information tables, and much more; to allow meaningful, valued exchanges and social interaction.

Last Updated: 29 Mar 2015

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How do you compare to others with this condition?

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Retroperitoneal fibrosis" for support, advocacy or research.

Logo
Retroperitoneal Fibrosis World Support

We offer both a warm and comforting welcome and an unrivaled learning experience to build self awareness of RF. We welcome all patients, caregivers, family, friends, and interested medical professionals. This forum is for each member to offer others moral support, friendship, and opinions and advice based on our personal experiences with RF This group includes access to unsurpassed resources of professional papers, case histories, files, relevant links, a member recommended doctor database, information tables, and much more; to allow meaningful, valued exchanges and social interaction.

https://groups.yahoo.com/neo/groups/retroperitoneal_fibrosisworldsuppo ...

Last Updated: 29 Mar 2015

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Retroperitoneal fibrosis" returned 209 free, full-text research articles on human participants. First 3 results:

About a case of unilateral perirenal retroperitoneal fibrosis without aorta involvement.
 

Author(s): C Alberti

Journal: Eur Rev Med Pharmacol Sci. 2015 Apr;19(7):1119-20.

 

Last Updated: 27 Apr 2015

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Retroperitoneal fibrosis: a retrospective clinical data analysis of 30 patients in a 10-year period.
 

Author(s): Hai-Jiang Zhou, Yong Yan, Biao Zhou, Tian-Fei Lan, Xue-Yan Wang, Chun-Sheng Li

Journal: Chin. Med. J.. 2015 Mar;128(6):804-10.

 

Retroperitoneal fibrosis (RPF) is an uncommon disease that is characterized by development of fibrosclerotic tissues involving retroperitoneal structures. This study aimed to investigate the clinical features of 30 patients with RPF in a single center in Beijing in a 10-year period.

Last Updated: 11 Mar 2015

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[Retroperitoneal fibrosis associated with malignancies: report of eight cases].
 

Author(s): Jorge Vega, Alejandro Ceriani, Daniela Jensen

Journal: Rev Med Chil. 2014 Jun;142(6):791-8.

 

Retroperitoneal fibrosis (RPF) is uncommon. Eight percent of cases are associated with malignancies. The pathogenesis of cancer related RPF (MRPF) is unknown. It may be originated from a desmoplastic reaction of the retroperitoneum to the presence of malignant cells, to the action ...

Last Updated: 20 Oct 2014

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Retroperitoneal fibrosis" returned 18 free, full-text review articles on human participants. First 3 results:

[Clinical characteristics of IgG4 related retroperitoneal fibrosis: a report of 5 cases and literature review].
 

Author(s): Yao-jun Dun, Lu-ping Yu, Yi-qing Du, Zheng-zuo Sheng, Gong-wei Wang, Xue Li, Bing Yang, Tao Xu, Xiao-bo Huang, Xiao-feng Wang

Journal: Beijing Da Xue Xue Bao. 2015 Aug;47(4):622-7.

 

To explore the clinical characteristics, treatment and prognosis of IgG4-related retroperitoneal fibrosis (RPF).

Last Updated: 19 Aug 2015

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Idiopathic and secondary forms of retroperitoneal fibrosis: a diagnostic approach.
 

Author(s): M L Urban, A Palmisano, M Nicastro, D Corradi, C Buzio, A Vaglio

Journal: Rev Med Interne. 2015 Jan;36(1):15-21.

 

Retroperitoneal fibrosis (RPF) is an uncommon disease characterized by a fibrous reaction that takes place in the peri-aortic retroperitoneum and often entraps the ureters causing obstructive uropathy. RPF is idiopathic in the majority of cases, but can also be secondary to malignancies, ...

Last Updated: 22 Dec 2014

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[Idiopathic retroperitoneal fibrosis misdiagnosed as renal cancer: a case report and literature review].
 

Author(s): Weining Wang, Yanbo Wang, Xiaobo Ma, Haidong Yu, Chunxi Wang

Journal: Nan Fang Yi Ke Da Xue Xue Bao. 2014 Nov;34(11):1658-60.

 

A 51-year-old male patient was presented to our hospital for inspection of right renal space-occupying lesions. CT revealed soft tissue density in the right renal pelvis and renal pelvis ureter transitional crumb, for which a clinical diagnosis of right renal cancer was made. After ...

Last Updated: 21 Nov 2014

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Symptoms, Diagnosis, and Treatment

There are currently no related results available in Genetics Home Reference.

There are currently no related results available in GeneReviews.

There are currently no related results available in Genetic Testing Registry.

 
 
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Clinical Trial Information This information is provided by ClinicalTrials.gov

Methotrexate as a Steroid-sparing Agent in Idiopathic Retroperitoneal Fibrosis: a Randomised, Multicenter Trial
 

Status: Recruiting

Condition Summary: Idiopathic Retroperitoneal Fibrosis; Perianeurysmal Retroperitoneal Fibrosis; Chronic Periaortitis

 

Last Updated: 12 Nov 2010

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Leflunomide for Maintenance of Remission in IgG4 Related Disease
 

Status: Recruiting

Condition Summary: Immunoglobulin G4 Related Sclerosing Disease

 

Last Updated: 30 Mar 2016

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