Retroperitoneal fibrosis

Common Name(s)

Retroperitoneal fibrosis, Ormond's Disease

Retroperitoneal fibrosis is a slowly progressive disorder in which the tubes that carry urine from the kidneys to the bladder (ureters) and other abdominal organs are blocked by a fibrous mass and inflammation in the back of the abdomen. The disorder may cause chronic unilateral obstructive uropathy or chronic bilateral obstructive uropathy. Risk factors for retroperitoneal fibrosis include asbestos exposure, smoking, tumor, infection, trauma, radiotherapy, surgery, and use of certain drugs.
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Retroperitoneal fibrosis" for support, advocacy or research.

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Retroperitoneal Fibrosis World Support

We offer both a warm and comforting welcome and an unrivaled learning experience to build self awareness of RF. We welcome all patients, caregivers, family, friends, and interested medical professionals. This forum is for each member to offer others moral support, friendship, and opinions and advice based on our personal experiences with RF This group includes access to unsurpassed resources of professional papers, case histories, files, relevant links, a member recommended doctor database, information tables, and much more; to allow meaningful, valued exchanges and social interaction.

Last Updated: 29 Mar 2015

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General Support Organizations

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How do you compare to others with this condition?

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Retroperitoneal fibrosis" for support, advocacy or research.

Logo
Retroperitoneal Fibrosis World Support

We offer both a warm and comforting welcome and an unrivaled learning experience to build self awareness of RF. We welcome all patients, caregivers, family, friends, and interested medical professionals. This forum is for each member to offer others moral support, friendship, and opinions and advice based on our personal experiences with RF This group includes access to unsurpassed resources of professional papers, case histories, files, relevant links, a member recommended doctor database, information tables, and much more; to allow meaningful, valued exchanges and social interaction.

https://groups.yahoo.com/neo/groups/retroperitoneal_fibrosisworldsuppo ...

Last Updated: 29 Mar 2015

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Retroperitoneal fibrosis" returned 211 free, full-text research articles on human participants. First 3 results:

Idiopathic retroperitoneal fibrosis causing unilateral ureteral and sigmoid colon obstruction: A case report.
 

Author(s): Ting Yan, Yujuan Wang, Zhijun Liu, Xiaolei Zhang, Qian Wu, Mingrong Xi

Journal: Medicine (Baltimore). 2017 Feb;96(7):e6105.

 

The present report aimed to present a unique case of idiopathic retroperitoneal fibrosis (RPF) presenting features of unilateral ureteral and sigmoid colon obstruction. RPF is a rare disorder with unclear etiology.

Last Updated: 16 Feb 2017

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IgG4-related retroperitoneal fibrosis: A case report and review of literature.
 

Author(s): Azra Niaz, Asad Hayat Ahmad, , Muhammed Ahmad Saeed, Omer Sabir, Nauman Tarif

Journal: J Pak Med Assoc. 2016 Feb;66(2):220-2.

 

Idiopathic Retroperitoneal fibrosis is a rare clinical condition recently identified as an autoimmune process related to Immunoglobulin G4 (IgG4) deposition. Herein we report a case of a 46 year old male presenting with 4 months history of backache, fever, flank pain and leg swelling ...

Last Updated: 28 Jan 2016

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Retroperitoneal Metastasis from Lung Adenocarcinoma Mimics Retroperitoneal Fibrosis.
 

Author(s): Akihiro Nishiyama, Hiroshige Yoshioka, Satoshi Ikeo, Mitsunori Morita, Naoyuki Sone, Satoshi Ikeda, Toshihide Yokoyama, Tadashi Ishida

Journal: J Thorac Oncol. 2016 Feb;11(2):266-7.

 

Last Updated: 26 Jan 2016

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Retroperitoneal fibrosis" returned 19 free, full-text review articles on human participants. First 3 results:

Overlap of Post-obstructive Diuresis and Unmasked Diabetes Insipidus in a Case of IgG4-related Retroperitoneal Fibrosis and Tuberoinfundibular Hypophysitis: A Case Report and Review of the Literature.
 

Author(s): Midori Sasaki Yatabe, Kimio Watanabe, Yoshimitsu Hayashi, Junichi Yatabe, Satoshi Morimoto, Atsuhiro Ichihara, Masaaki Nakayama, Tsuyoshi Watanabe

Journal: Intern. Med.. ;56(1):47-53.

 

The clinical picture of IgG4-related disease (IgG4-RD) is diverse because various organs can be affected. We describe the case of a 56-year-old man with acute renal failure and tuberoinfundibular hypophysitis due to IgG4-RD. Steroid therapy lowered the serum IgG4 level and ameliorated ...

Last Updated: 4 Jan 2017

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[Clinical characteristics of IgG4 related retroperitoneal fibrosis: a report of 5 cases and literature review].
 

Author(s): Yao-jun Dun, Lu-ping Yu, Yi-qing Du, Zheng-zuo Sheng, Gong-wei Wang, Xue Li, Bing Yang, Tao Xu, Xiao-bo Huang, Xiao-feng Wang

Journal: Beijing Da Xue Xue Bao. 2015 Aug;47(4):622-7.

 

To explore the clinical characteristics, treatment and prognosis of IgG4-related retroperitoneal fibrosis (RPF).

Last Updated: 19 Aug 2015

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Idiopathic and secondary forms of retroperitoneal fibrosis: a diagnostic approach.
 

Author(s): M L Urban, A Palmisano, M Nicastro, D Corradi, C Buzio, A Vaglio

Journal: Rev Med Interne. 2015 Jan;36(1):15-21.

 

Retroperitoneal fibrosis (RPF) is an uncommon disease characterized by a fibrous reaction that takes place in the peri-aortic retroperitoneum and often entraps the ureters causing obstructive uropathy. RPF is idiopathic in the majority of cases, but can also be secondary to malignancies, ...

Last Updated: 22 Dec 2014

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Symptoms, Diagnosis, and Treatment

There are currently no related results available in GeneReviews.

There are currently no related results available in Genetic Testing Registry.

 
 
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Clinical Trial Information This information is provided by ClinicalTrials.gov

Treatment of IgG4-Related Disease With Revlimid and Rituximab
 

Status: Recruiting

Condition Summary: Immunoglobulin G Subclass 4 Related Disease; IgG4-related Disease; Autoimmune Pancreatitis; IgG4-related Sclerosing Cholangitis; Retroperitoneal Fibrosis

 

Last Updated: 12 Sep 2016

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Leflunomide for Maintenance of Remission in IgG4 Related Disease
 

Status: Recruiting

Condition Summary: Immunoglobulin G4 Related Sclerosing Disease

 

Last Updated: 30 Mar 2016

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