Pulmonary sequestration

Common Name(s)

Pulmonary sequestration

Pulmonary sequestration is a rare malformation where non-functioning lung tissue is separated from the rest of the lung and supplied with blood from an unusual source, often an artery from systemic circulation.  It may be congenital (present from birth) or acquired. Pulmonary sequestrations may be defined as intralobular or extralobular, depending on their location. Symptoms may include chronic cough, respiratory distress or infection. Treatment depends on the location and may involve surgery.
 

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Pulmonary sequestration" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Pulmonary sequestration" returned 95 free, full-text research articles on human participants. First 3 results:

Intradiaphragmatic extralobar pulmonary sequestration in adult.
 

Author(s): Jang-Hoon Lee, Mi-Jin Kim

Journal:

 

Extralobar pulmonary sequestrations may be located in intrathoracic or extrathoracic areas. Extrathoracic intradiaphragmatic extralobar pulmonary sequestrations are an extremely rare subset of bronchopulmonary sequestrations and there have been very few reported cases until now. We ...

Last Updated: 1 Jul 2014

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Immunohistochemical analyses of a case of extralobar pulmonary sequestration with chest pain in an adult.
 

Author(s): Yuji Ohtsuki, Masashi Uomoto, Yasuki Hachisuka, Mutsuo Furihata

Journal: Indian J Pathol Microbiol. ;56(4):434-6.

 

Computed tomography of a Japanese man in his mid-forties with a complaint of right-side chest pain showed a dome-shaped smooth-surfaced mediastinal mass, which was extirpated. The cut surface was highly hemorrhagic and necrotic and not related to the original pulmonary tissues. Although ...

Last Updated: 20 Jan 2014

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Pulmonary sequestration presented as massive left hemothorax and associated with primary lung sarcoma.
 

Author(s): Vincenzo Di Crescenzo, Paolo Laperuta, Filomena Napolitano, Chiara Carlomagno, Alfredo Garzi, Mario Vitale

Journal: BMC Surg. 2013 ;13 Suppl 2():S34.

 

Pulmonary sequestration is an uncommon disease, accounting for only approximately 1.5% of all congenital pulmonary malformations. In most cases, the diagnosis is a result of accidental radiological findings; it is rarely accompanied by clinical symptoms, and is more commonly associated ...

Last Updated: 25 Nov 2013

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Pulmonary sequestration" returned 7 free, full-text review articles on human participants. First 3 results:

Bilateral pulmonary sequestration in an adult: case report and review of the literature.
 

Author(s): Montserrat Fontalba Navas, Justo Sánchez Gil, José Calvo Bonachera

Journal: Arch. Bronconeumol.. 2013 Sep;49(9):410-1.

 

Last Updated: 9 Sep 2013

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Surgical treatment of infected intralobar pulmonary sequestration: a collective review of patients older than 50 years reported in the literature.
 

Author(s): Shinji Hirai, Yoshiharu Hamanaka, Norimasa Mitsui, Shinnosuke Uegami, Yousuke Matsuura

Journal: Ann Thorac Cardiovasc Surg. 2007 Oct;13(5):331-4.

 

We report on the rare and surgical treatment of a senile patient of infected intralobar pulmonary sequestration. A 56-year-old male who had complained of headache, vomiting, cough, sputum production, and high fever was admitted to our hospital. Chest computed tomography (CT) showed ...

Last Updated: 23 Oct 2007

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Prenatal detection and evaluation of an extralobar pulmonary sequestration in the posterior mediastinum.
 

Author(s): D York, A Swartz, A Johnson, J Fielding, J D Phillips

Journal: Ultrasound Obstet Gynecol. 2006 Feb;27(2):214-6.

 

Extralobar pulmonary sequestration (EPS) is a rare developmental anomaly with aberrant nonfunctioning parenchymal tissue, associated with an increased risk of perinatal morbidity and, rarely, mortality owing to possible neonatal respiratory distress. In most cases supernumerary lobes ...

Last Updated: 31 Jan 2006

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Symptoms, Diagnosis, and Treatment

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Clinical Trial Information This information is provided by ClinicalTrials.gov

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