Pulmonary Lymphangiomatosis

Common Name(s)

Pulmonary Lymphangiomatosis

Pulmonary lymphangiomatosis, or simply lymphangiomatosis, is a rare disorder that is believed to be congenital (people are born with it) and can affect any of the body's systems except the central nervous system (including the brain). It is a disease of the lymphatic system, which is a network of vessels that circulate fluid besides blood through the rest of the body and also work as part of the body's immune system. Pulmonary lymphangiomatosis can affect anyone at any age, but it is most commonly diagnosed in children and almost always before age 20. Symptoms include chest pain and pressure, coughing up blood and shortness of breath. Talk with your doctor to find the best treatment if you or your child has been diagnosed with pulmonary lymphangiomatosis.

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Pulmonary Lymphangiomatosis" for support, advocacy or research.

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How do you compare to others with this condition?

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Pulmonary Lymphangiomatosis" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Pulmonary Lymphangiomatosis" returned 9 free, full-text research articles on human participants. First 3 results:

Diffuse pulmonary lymphangiomatosis.
 

Author(s): Kunal C Kadakia, Sandeep M Patel, Eunhee S Yi, Andrew H Limper

Journal: Can. Respir. J.. ;20(1):52-4.

 

Diffuse pulmonary lymphangiomatosis (DPL) is a rare disease characterized by infiltration of the lung, pleura and mediastinum with thin-walled lymphangiomas. DPL can result in mass effect from infiltrative disease, restrictive and obstructive pulmonary physiology, chylous effusions ...

Last Updated: 4 Mar 2013

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Pulmonary lymphangiomatosis.
 

Author(s): Melissa N Satria, Gustavo Pacheco-Rodriguez, Joel Moss

Journal: Lymphat Res Biol. 2011 ;9(4):191-3.

 

Lymphangiomatosis is a rare disease characterized by diffuse infiltration of lymphangiomas in the lung, bone, and other tissues. Due to its rarity, the spectrum of lymphangiomatosis is beginning to be elucidated based on case reports. The limited pathological, radiological, and clinical ...

Last Updated: 26 Dec 2011

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Diffuse pulmonary lymphangiomatosis with mediastinal affectation.
 

Author(s): Y Caballero, D PĂ©rez, J R Cano

Journal: Arch. Bronconeumol.. 2011 Sep;47(9):474-5.

 

Last Updated: 9 Sep 2011

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Pulmonary Lymphangiomatosis" returned 2 free, full-text review articles on human participants. First 3 results:

A rare case of diffuse pulmonary lymphangiomatosis in a middle-aged woman.
 

Author(s): Hyun-ju Lim, Joungho Han, Hong Kwan Kim, Tae Sung Kim

Journal: Korean J Radiol. ;15(2):295-9.

 

Diffuse pulmonary lymphangiomatosis (DPL) is a rare lymphatic disorder characterized by lymphatic channel proliferation. It is mostly reported in children and young adults. Here, we report a case involving a 52-year-old asymptomatic woman who presented with increased interstitial ...

Last Updated: 19 Mar 2014

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Diffuse pulmonary lymphangiomatosis: a case report with literature review.
 

Author(s): Ming-Hua DU, Ruan-Jian Ye, Kun-Kun Sun, Jian-Feng Li, Dan-Hua Shen, Jun Wang, Zhan-Cheng Gao

Journal: Chin. Med. J.. 2011 Mar;124(5):797-800.

 

Diffuse pulmonary lymphangiomatosis (DPL) is a rare disease that is characterized by diffuse proliferation of abnormal pulmonary lymphatic channels. DPL occurs mostly in children and young adults and often undergoes a progressive clinical course, eventually causing deterioration of ...

Last Updated: 26 Apr 2011

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Symptoms, Diagnosis, and Treatment

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Clinical Trial Information This information is provided by ClinicalTrials.gov

Characterization of the Pathogenesis of Primary and Secondary Lymphatic Disorders
 

Status: Recruiting

Condition Summary: Lymphangiomatosis; Lymphedema; Lymphangiectasia; Pulmonary Lymphangiectasia

 

Last Updated: 4 Jun 2014

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