Pulmonary artery agenesis

Common Name(s)

Pulmonary artery agenesis

Pulmonary artery agenesis is an infrequent pulmonary arteriovenous malformation, an abnormality of the lung caused by abnormal communications between arteries and veins in the lungs. The disease is present at birth due to a malformation in the development of the heart. The condition may manifest with total or partial absence of the lung on the same side with the presence of an unusual contracting lung. In children, the affected side of the chest is usually decreased in size, with a reduction in inspiratory amplitude and diminished breath sounds.

Pulmonary artery agenesis is usually well tolerated and manifests with repeated infections and chest pain, among other symptoms. Tolerance becomes complicated if the condition is moreover associated to compression of vessels carrying blood or other malformations.

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Pulmonary artery agenesis" for support, advocacy or research.

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General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Pulmonary artery agenesis" returned 15 free, full-text research articles on human participants. First 3 results:

Incidentally detected right pulmonary artery agenesis with right coronary artery collateralization.
 

Author(s): Nino Mikaberidze, Ythan Goldberg, Khashayar Khosraviani, Cynthia Taub

Journal: Interact Cardiovasc Thorac Surg. 2014 Jan;18(1):139-40.

 

Unilateral pulmonary artery agenesis (UPAA) with pulmonary hypoplasia is a rare congenital anomaly. We describe a 71-year old male who was incidentally diagnosed with the right UPAA and a hypoplastic right lung supplied by collateralized right coronary.

Last Updated: 19 Dec 2013

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Eisenmenger's syndrome and agenesis of the right pulmonary artery: a case of double diagnosis.
 

Author(s): Bhanu Duggal, Ganesh Narayan

Journal: Cardiol J. 2013 ;20(1):103-5.

 

We present a case of patent ductus arteriosus with severe pulmonary hypertension with the rare association of absent right pulmonary artery.

Last Updated: 5 Apr 2013

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Pneumonectomy for congenital isolated unilateral pulmonary artery agenesis.
 

Author(s): J Britton, A Sachithanandan, L Srinivasan, S Ghosh

Journal: Med. J. Malaysia. 2011 Oct;66(4):363-4.

 

Unilateral pulmonary artery agenesis (UPAA) is a rare congenital anomaly usually diagnosed in infancy due to associated cardiovascular malformations. We report a rare case of isolated right UPAA that presented atypically in adulthood with massive haemoptysis requiring a pneumonectomy. ...

Last Updated: 3 Feb 2012

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Pulmonary artery agenesis" returned 0 free, full-text review articles on human participants.

 
 
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Symptoms, Diagnosis, and Treatment

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Clinical Trial Information This information is provided by ClinicalTrials.gov

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