Hemangioendothelioma

Common Name(s)

Hemangioendothelioma

The term hemangioendothelioma describes several types of vascular neosplasms and includes both non-cancerous (benign) and cancerous (malignant) growths. The term has also been applied to those that show "borderline" behavior, intermediate between entirely benign hemangiomas and highly malignant angiosarcomas. Hemangioendotheliomas are caused by abnormal growth of blood vessel cells, although the exact underlying cause for the abnormal growth is unknown. They can also develop in an organ, such as the liver or lung. They usually grow slowly and can sometimes spread to other tissues in the body (metastasize). Examples of types of hemangioendotheliomas include spindle cell hemangioma; papillary intralymphatic (Dabska tumor); retiform; kaposiform; epithelioid; pseudomyogenic (epithelioid sarcoma-like hemangioendothelioma); and composite. Treatment depends on the type of hemangioendothelioma present but typically includes surgical excision (removal).
 

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Hemangioendothelioma" for support, advocacy or research.

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Hemangioendothelioma" returned 187 free, full-text research articles on human participants. First 3 results:

Intestinal obstruction due to kaposiform hemangioendothelioma in a 1-month-old infant: A case report.
 

Author(s): Joong Kee Youn, Shin-Hoo Park, Ji-Won Han, Chaeyoun Oh, Hyun-Young Kim, Sung-Eun Jung

Journal: Medicine (Baltimore). 2017 Sep;96(37):e6974.

 

Kaposiform hemangioendothelioma (KHE) is an aggressive vascular tumor, mainly occurring in infants and young children and previously reported cases were mainly cutaneous or visceral form. Intestinal kaposiform hemangioma was first reported in 2012. Intestinal type KHE showed better ...

Last Updated: 14 Sep 2017

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The clinical features of epithelioid hemangioendothelioma in a Han Chinese population: A retrospective analysis.
 

Author(s): Qinyue Guo, Jing Xue, Lin Xu, Zhihong Shi, Bo Zhou

Journal: Medicine (Baltimore). 2017 Jun;96(26):e7345.

 

Epithelioid hemangioendothelioma (EHE) is a rare indolent vascular tumor which occurs at liver, lung, bone, and so on. However, the etiology of EHE is evasive.These patients were enrolled at the First Affiliated Hospital of Xi'an Jiaotong University from January 2011 to December 2015. ...

Last Updated: 28 Jun 2017

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Epithelioid hemangioendothelioma of right innominate vein mimics a teratoma: A case report.
 

Author(s): Qi Wan, Jiaxuan Zhou, Yudong Yu, Qingyu Sun, Yingying Bao, Qiang Lei, Qiao Zou, Yingshi Deng, Xinchun Li

Journal: Medicine (Baltimore). 2017 Mar;96(9):e6142.

 

Epithelioid hemangioendothelioma (EHE) is a rare neoplasm commonly known to arise from the soft tissue, lung, and liver. EHE arising from right innominate vein (RIV) has scarcely been reported in English literature.

Last Updated: 1 Mar 2017

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Hemangioendothelioma" returned 24 free, full-text review articles on human participants. First 3 results:

Spontaneous rupture of hepatic epithelioid hemangioendothelioma: A case report.
 

Author(s): Jun-Wu Yang, Yong Li, Kai Xie, Wei Dong, Xian-Tong Cao, Wei-Dong Xiao

Journal: World J. Gastroenterol.. 2017 Jan;23(1):185-190.

 

Hepatic epithelioid hemangioendothelioma (HEH) is a rare tumor of vascular endothelial origin. Spontaneous rupture of HEH is a life-threatening complication and is extremely rare. HEH has variable malignant potential, and the clinical diagnosis remains challenging. Here we report ...

Last Updated: 20 Jan 2017

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Recurrence of Epithelioid Hemangioendothelioma during Pregnancy: Case Report and Systematic Review.
 

Author(s): Michael Mcculloch, Michael Russin, Arian Nachat

Journal: Perm J. 2016 ;20(3):84-9.

 

Epithelioid hemangioendothelioma (EHE) is a family of blood vessel tumors originating in blood vessels, bone, brain, kidney, liver, and lung. EHE is more common in women, and chemotherapy, radiation, and surgery have brought few successes.

Last Updated: 20 Aug 2016

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A case report of retiform hemangioendothelioma as pleural nodules with literature review.
 

Author(s): Qingqing Liu, Ruoyun Ouyang, Ping Chen, Rui Zhou

Journal:

 

Retiform hemangioendothelioma (RH) is a rare low-grade variant of angiosarcoma mostly reported on dermis or subcutaneously. A 30-year-old woman suffering from dry cough, dyspnea and pleural effusion has been described. Distinctive symptoms and lesions on high resolution computed tomography ...

Last Updated: 27 Oct 2015

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Symptoms, Diagnosis, and Treatment

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Clinical Trial Information This information is provided by ClinicalTrials.gov

Last Updated: 25 Sep 2017

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Sirolimus Versus Sirolimus Plus Prednisolone for Kaposiform Hemangioendothelioma With Kasabach-Merritt Syndrome
 

Status: Recruiting

Condition Summary: Kaposiform Hemangioendothelioma; Kasabach Merritt Phenomenon

 

Last Updated: 15 Jun 2017

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A Study to Compare Vincristine to Sirolimus for Treatment of High Risk Vascular Tumors
 

Status: Recruiting

Condition Summary: Kaposiform Hemangioendothelioma (KHE); Kasabach-Merritt Syndrome; Tufted Angioma

 

Last Updated: 11 Jul 2017

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