Febrile Ulceronecrotic Mucha-Habermann Disease

Common Name(s)

Febrile Ulceronecrotic Mucha-Habermann Disease

Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare and severe form of pityriasis lichenoides et varioliformis acuta (PLEVA). PLEVA is characterized by skin lesions that ulcerate, breakdown, form open sores, then form a red-brown crust. FUMHD often begins as PLEVA, but then rapidly and suddenly progresses to large, destructive ulcers. There may be fever and extensive, painful loss of skin tissue as well as secondary infection of the ulcers. Diagnosis of FUMHD is confirmed by biopsy of skin lesions. FUMHD occurs more frequently in children, peaking at age 5 to 10. Males tend to be affected more often than females. While some cases of FUMHD have resolved without therapy, others have resulted in death. Early diagnosis and prompt treatment may help to reduce morbidity and death.
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Febrile Ulceronecrotic Mucha-Habermann Disease" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

Not finding the support you need? Show General Support Organizations

 
 
Top

How do you compare to others with this condition?

Privately answer questions about your health. Let resources, you select, come to you.

Anonymously share and see how your answers compare with others with this condition while privately providing key pieces of information to medical researchers, disease advocacy groups, and others ONLY YOU select to help speed up cures and better alternatives.

 
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Febrile Ulceronecrotic Mucha-Habermann Disease" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

Not finding the support you need? Show General Support Organizations

 
 
 
 
Top

Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Febrile Ulceronecrotic Mucha-Habermann Disease" returned 3 free, full-text research articles on human participants. First 3 results:

Febrile ulceronecrotic Mucha-Habermann disease in adult patient successfully treated with systemic corticosteroid.
 

Author(s): Priscila Wolf Nassif, Deise Aparecida Santos Godoy, Sadamitsu Nakandakari, Cinthia Janine Meira Alves, Cleverson Teixeira Soares

Journal: An Bras Dermatol. ;85(6):891-4.

 

The Febrile Ulceronecrotic Mucha-Habermann (FUMHD) disease is a rare variant of pityriasis lichenoides et varioliformis acuta (PLEVA). Its etiology still remains unknown and it is characterized by a sudden onset of ulceronecrotic skin lesions associated with systemic symptoms. It ...

Last Updated: 10 Feb 2011

Go To URL
[Febrile ulceronecrotic Mucha-Habermann disease with exuberant mucosal involvement: case report].
 

Author(s): Moema Mignac Cumming, Adriana S Salathiel, Mário Alberto S Paino, Sérgio Delort, Ana Maria Roselino

Journal: An Bras Dermatol. ;84(6):655-8.

 

Pityriasis lichenoides is a rare idiopathic cutaneous disorder, with a clinical-histopathological spectrum comprising the acute varioliform form (Mucha-Habermann's disease), its febrile ulceronecrotic variant, and its chronic form. Systemic manifestations may occur in the febrile ...

Last Updated: 1 Mar 2010

Go To URL
Febrile ulceronecrotic Mucha Habermann disease: a fatality.
 

Author(s): M A Hoghton, J P Ellis, M J Hayes

Journal: J R Soc Med. 1989 Aug;82(8):500-1.

 

Last Updated: 18 Oct 1989

Go To URL

Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Febrile Ulceronecrotic Mucha-Habermann Disease" returned 3 free, full-text review articles on human participants. First 3 results:

Febrile ulceronecrotic Mucha-Habermann disease: a case report and review of the literature.
 

Author(s): Eleni Sotiriou, Aikaterini Patsatsi, Christina Tsorova, Elisabeth Lazaridou, Dimitrios Sotiriadis

Journal: Acta Derm. Venereol.. 2008 ;88(4):350-5.

 

Febrile ulceronecrotic Mucha-Habermann disease is a severe variant of pityriasis lichenoides et varioliformis acuta characterized by the sudden onset of ulceronecrotic skin lesions and associated with high fever and systemic symptoms. We report here a case of a 20-year-old woman in ...

Last Updated: 18 Aug 2008

Go To URL
Febrile ulceronecrotic Mucha-Habermann disease: a case report and a review of the literature.
 

Author(s): Sema Aytekin, Gokcen Balci, Ozgur Yagdiran Duzgun

Journal:

 

We report a case of febrile ulceronecrotic Mucha-Habermann disease (FUMHD) in a 27-year-old woman. After 20 days of a mild eruption, extensive polymorphous, papular and ulcerohemorrhagic skin lesions gradually developed, associated with intermittent high temperature, and constitutional ...

Last Updated: 13 Jan 2006

Go To URL
Febrile ulceronecrotic Mucha-Habermann disease: a case report and a review of the literature.
 

Author(s): T Miyamoto, N Takayama, S Kitada, Y Hagari, M Mihara

Journal: J. Clin. Pathol.. 2003 Oct;56(10):795-7.

 

This report describes the case of a 76 year old man who suffered from febrile ulceronecrotic Mucha-Habermann disease (FUMHD). Despite this patient's typical clinical and histological findings, the fulminating course led to death. Polymerase chain reaction (PCR) analysis of the skin ...

Last Updated: 29 Sep 2003

Go To URL
 
 
Top

Symptoms, Diagnosis, and Treatment

There are currently no related results available in Genetics Home Reference.

There are currently no related results available in GeneReviews.

There are currently no related results available in Genetic Testing Registry.

 
 
Top

Clinical Trial Information This information is provided by ClinicalTrials.gov

There are currently no open clinical trials for this condition.