Aggressive Fibromatosis

Common Name(s)

Aggressive Fibromatosis

Description for this condition is not yet available.
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Aggressive Fibromatosis" for support, advocacy or research.

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The Desmoid Tumor Research Foundation

Dedicated to funding research to find a cure for desmoid tumors

Last Updated: 19 Feb 2013

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General Support Organizations

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How do you compare to others with this condition?

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Aggressive Fibromatosis" for support, advocacy or research.

Logo
The Desmoid Tumor Research Foundation

Dedicated to funding research to find a cure for desmoid tumors

http://www.dtrf.org

Last Updated: 19 Feb 2013

View Details

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Aggressive Fibromatosis" returned 40 free, full-text research articles on human participants. First 3 results:

Desmoid tumor of lung with pleural involvement - the case of unique location of aggressive fibromatosis.
 

Author(s): Tomasz Tokarek, Joanna Szpor, Juliusz Pankowski, Krzysztof Okoń

Journal: Folia Med Cracov. 2015 ;55(1):53-9.

 

Desmoid tumors (DTs) are rare mesenchymal neoplasms with unpredictable natural history. There is a high risk of recurrence despite adequate surgical resection, however DTs do not have the capacity to metastasize. The estimated incidence in general population is 2-4 cases/million/year. ...

Last Updated: 18 Jan 2016

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Time trends in the incidence and treatment of extra-abdominal and abdominal aggressive fibromatosis: a population-based study.
 

Author(s): Danique L M van Broekhoven, Dirk J Grünhagen, Michael A den Bakker, Thijs van Dalen, Cornelis Verhoef

Journal: Ann. Surg. Oncol.. 2015 Sep;22(9):2817-23.

 

Aggressive fibromatosis (AF) is a locally infiltrating soft-tissue tumor. In a population-based study in the Netherlands, we evaluated time trends for the incidence and treatment of AF.

Last Updated: 11 Aug 2015

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Aggressive fibromatosis of the leg and sacrococcygeal region: a report of two cases.
 

Author(s): Fuwen Pan, Qiang Liu, Guoru Zhang, Qiqi Wang, Bo Yun, Yaoguang Han, Rui Deng, Linqing Wu, Shihua Wang

Journal:

 

Aggressive fibromatosis is a rare soft tissue tumor that composes of myofibroblasts that arise from musculoaponeurotic structures. It usually affects the abdominal wall but may be also found in other less common sites including the head and neck, submucosa of the oral cavity, spinal, ...

Last Updated: 10 Mar 2015

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Aggressive Fibromatosis" returned 3 free, full-text review articles on human participants. First 3 results:

Locally Aggressive De Novo Spinal Fibromatosis: Case Report and Review of the Literature.
 

Author(s): Murat Sakir Eksi, Huseyin Kemal Turkoz, Emel Eksi, Akın Akakin, Zafer Orkun Toktas, Deniz Konya

Journal: Turk Neurosurg. 2015 ;25(5):818-23.

 

Fibromatosis is a benign lesion, which originates from proliferating fibroblasts. Although fibromatosis is a benign tumor, it is locally aggressive and invasive. Spinal presentation of fibromatosis is very rare, and case reports are the only source of the clinical knowledge. Herein, ...

Last Updated: 7 Oct 2015

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Pediatric aggressive fibromatosis: a retrospective analysis of 13 patients and review of literature.
 

Author(s): Saskia Buitendijk, Cees P van de Ven, Ton G Dumans, Jan C den Hollander, Peter J Nowak, Wim J Tissing, Rob Pieters, Marry M van den Heuvel-Eibrink

Journal: Cancer. 2005 Sep;104(5):1090-9.

 

Aggressive fibromatosis (AF) is a soft tissue tumor and is rare in childhood, with high potential for local invasiveness and recurrence. General recommendations for the clinical management of pediatric patients with AF remain undetermined.

Last Updated: 29 Aug 2005

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The pharmacological treatment of aggressive fibromatosis: a systematic review.
 

Author(s): J Janinis, M Patriki, L Vini, G Aravantinos, J S Whelan

Journal: Ann. Oncol.. 2003 Feb;14(2):181-90.

 

Despite the use of surgery and radiotherapy, 20-35% of patients with aggressive fibromatosis (AF) will have local recurrence. The purpose of this review was to collect and analyze all available information regarding the role of non-cytotoxic and cytotoxic chemotherapy in AF that has ...

Last Updated: 3 Feb 2003

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Symptoms, Diagnosis, and Treatment

There are currently no related results available in Genetics Home Reference.

There are currently no related results available in GeneReviews.

There are currently no related results available in Genetic Testing Registry.

 
 
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Clinical Trial Information This information is provided by ClinicalTrials.gov

National Clinical-biological Prospective Cohort of Incident Cases of Aggressive Fibromatosis (ALTITUDES)
 

Status: Recruiting

Condition Summary: Aggressive Fibromatosis

 

Last Updated: 16 Aug 2016

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Last Updated: 9 May 2016

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PAZOPANIB Efficacy and Tolerance in Desmoids Tumors
 

Status: Recruiting

Condition Summary: Progressive Desmoids Tumors

 

Last Updated: 25 May 2016

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