Aggressive Fibromatosis

Common Name(s)

Aggressive Fibromatosis

Description for this condition is not yet available.
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Aggressive Fibromatosis" for support, advocacy or research.

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The Desmoid Tumor Research Foundation

Dedicated to funding research to find a cure for desmoid tumors

Last Updated: 19 Feb 2013

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General Support Organizations

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Aggressive Fibromatosis" for support, advocacy or research.

Logo
The Desmoid Tumor Research Foundation

Dedicated to funding research to find a cure for desmoid tumors

http://www.dtrf.org

Last Updated: 19 Feb 2013

View Details

 

General Support Organizations

Not finding the support you need? Show General Support Organizations

 
 
 
 
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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Aggressive Fibromatosis" returned 45 free, full-text research articles on human participants. First 3 results:

Aggressive fibromatosis of the oral cavity in a 5 year old boy: a rare case report.
 

Author(s): Keerthi Krishnankutty Nair, Kanad Chaudhuri, Ashok Lingappa, Ranjani Shetty, Pramod Gujjar Vittobarao

Journal:

 

Fibrous tissue proliferations express a wide spectrum of histologic and morphologic variation in both infants and adults. This ranges from hypertrophic scar formation at one end to malignant fibrosarcoma at the other end of the spectrum. Aggressive fibromatosis is an intermediate ...

Last Updated: 31 Dec 1969

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Clinical Activity of the γ-Secretase Inhibitor PF-03084014 in Adults With Desmoid Tumors (Aggressive Fibromatosis).
 

Author(s): Shivaani Kummar, Geraldine O'Sullivan Coyne, Khanh T Do, Baris Turkbey, Paul S Meltzer, Eric Polley, Peter L Choyke, Robert Meehan, Rasa Vilimas, Yvonne Horneffer, Lamin Juwara, Ann Lih, Amul Choudhary, Sandra A Mitchell, Lee J Helman, James H Doroshow, Alice P Chen

Journal: J. Clin. Oncol.. 2017 May;35(14):1561-1569.

 

Purpose Desmoid tumors (aggressive fibromatosis) arise from connective tissue cells or fibroblasts. In general, they are slow growing and do not metastasize; however, locally aggressive desmoid tumors can cause severe morbidity and loss of function. Disease recurrence after surgery ...

Last Updated: 31 Dec 1969

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Pazopanib, a promising option for the treatment of aggressive fibromatosis.
 

Author(s): Zoltan Szucs, Christina Messiou, Han Hsi Wong, Helen Hatcher, Aisha Miah, Shane Zaidi, Winette T A van der Graaf, Ian Judson, Robin L Jones, Charlotte Benson

Journal: Anticancer Drugs. 2017 04;28(4):421-426.

 

Desmoid tumour/aggressive fibromatosis (DT/AF) is a rare soft-tissue neoplasm that is locally aggressive but does not metastasize. There is no standard systemic treatment for symptomatic patients, although a number of agents are used. Tyrosine kinase inhibitors have recently been ...

Last Updated: 31 Dec 1969

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Aggressive Fibromatosis" returned 3 free, full-text review articles on human participants. First 3 results:

Misdiagnosis of aggressive fibromatosis of the abdominal wall: A case report and literature review.
 

Author(s): Xiaoxia Liu, Shan Zong, Yingli Cui, Ying Yue

Journal: Medicine (Baltimore). 2018 Mar;97(10):e9925.

 

Aggressive fibromatosis (AF) of abdominal wall is also called desmoid tumor, ligament tumor, fibrous tissue tumor hyperplasia, tendon membrane fibroma or soft tissue ligament fibroma, etc. Aggressive fibromatosis of abdominal wall was first described by MacFarlane in 1832, and it ...

Last Updated: 31 Dec 1969

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Locally Aggressive De Novo Spinal Fibromatosis: Case Report and Review of the Literature.
 

Author(s): Murat Sakir Eksi, Huseyin Kemal Turkoz, Emel Eksi, Akın Akakin, Zafer Orkun Toktas, Deniz Konya

Journal: Turk Neurosurg. 2015 ;25(5):818-23.

 

Fibromatosis is a benign lesion, which originates from proliferating fibroblasts. Although fibromatosis is a benign tumor, it is locally aggressive and invasive. Spinal presentation of fibromatosis is very rare, and case reports are the only source of the clinical knowledge. Herein, ...

Last Updated: 31 Dec 1969

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Pediatric aggressive fibromatosis: a retrospective analysis of 13 patients and review of literature.
 

Author(s): Saskia Buitendijk, Cees P van de Ven, Ton G Dumans, Jan C den Hollander, Peter J Nowak, Wim J Tissing, Rob Pieters, Marry M van den Heuvel-Eibrink

Journal: Cancer. 2005 Sep;104(5):1090-9.

 

Aggressive fibromatosis (AF) is a soft tissue tumor and is rare in childhood, with high potential for local invasiveness and recurrence. General recommendations for the clinical management of pediatric patients with AF remain undetermined.

Last Updated: 31 Dec 1969

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Clinical Trial Information This information is provided by ClinicalTrials.gov

National Clinical-biological Prospective Cohort of Incident Cases of Aggressive Fibromatosis (ALTITUDES)
 

Status: Recruiting

Condition Summary: Aggressive Fibromatosis

 

Last Updated: 13 Oct 2017

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Last Updated: 5 Apr 2017

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PAZOPANIB Efficacy and Tolerance in Desmoids Tumors
 

Status: Recruiting

Condition Summary: Progressive Desmoids Tumors

 

Last Updated: 4 Oct 2017

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