Aggressive Fibromatosis

Common Name(s)

Aggressive Fibromatosis

Description for this condition is not yet available.
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Aggressive Fibromatosis" for support, advocacy or research.

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The Desmoid Tumor Research Foundation

Dedicated to funding research to find a cure for desmoid tumors

Last Updated: 19 Feb 2013

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General Support Organizations

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How do you compare to others with this condition?

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Aggressive Fibromatosis" for support, advocacy or research.

Logo
The Desmoid Tumor Research Foundation

Dedicated to funding research to find a cure for desmoid tumors

http://www.dtrf.org

Last Updated: 19 Feb 2013

View Details

 

General Support Organizations

Not finding the support you need? Show General Support Organizations

 
 
 
 
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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Aggressive Fibromatosis" returned 40 free, full-text research articles on human participants. First 3 results:

Five years of local control of subscapularis aggressive fibromatosis managed by surgery and imatinib: a case report.
 

Author(s): Abou Dao, Nadia Benchakroun, Hamza Jabir, Amina Taleb, Zineb Bouchbika, Nezha Tawfiq, Hassan Jouhadi, Souha Sahraoui, Abdellatif Benider

Journal:

 

Imatinib, a tyrosine kinase inhibitor, is a major therapeutic option for the management of unresectable aggressive fibromatosis. Unfortunately, for most patients of low or very low average income countries, surgery often is the first treatment option. This is related to unavailability ...

Last Updated: 8 Jan 2015

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The analysis of treatment of aggressive fibromatosis using oral methotrexate chemotherapy.
 

Author(s): Gi Woon Yoon, Jae Do Kim, So Hak Chung

Journal: Clin Orthop Surg. 2014 Dec;6(4):439-42.

 

Aggressive fibromatosis is a rare but invasive tumor infiltrating widely between fascia and muscle fibers. It has a high tendency to be locally recurrent despite complete resection. Effectiveness of adjuvant treatment for aggressive fibromatosis including radiotherapy, pharmacological ...

Last Updated: 1 Dec 2014

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Impact of KIT exon 10 M541L allelic variant on the response to imatinib in aggressive fibromatosis: analysis of the desminib series by competitive allele specific Taqman PCR technology.
 

Author(s): Armelle Dufresne, Laurent Alberti, Mehdi Brahmi, Sarah Kabani, Héloïse Philippon, David Pérol, Jean Yves Blay

Journal:

 

Aggressive fibromatosis (AF) is a rare fibroblastic proliferative disease with a locally aggressive behavior and no distant metastasis, characterized by driver mutations in CTNNB1 or the APC gene. When progressive and/or symptomatic AF is not amenable to local management, a variety ...

Last Updated: 9 Sep 2014

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Aggressive Fibromatosis" returned 2 free, full-text review articles on human participants. First 3 results:

Pediatric aggressive fibromatosis: a retrospective analysis of 13 patients and review of literature.
 

Author(s): Saskia Buitendijk, Cees P van de Ven, Ton G Dumans, Jan C den Hollander, Peter J Nowak, Wim J Tissing, Rob Pieters, Marry M van den Heuvel-Eibrink

Journal: Cancer. 2005 Sep;104(5):1090-9.

 

Aggressive fibromatosis (AF) is a soft tissue tumor and is rare in childhood, with high potential for local invasiveness and recurrence. General recommendations for the clinical management of pediatric patients with AF remain undetermined.

Last Updated: 29 Aug 2005

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The pharmacological treatment of aggressive fibromatosis: a systematic review.
 

Author(s): J Janinis, M Patriki, L Vini, G Aravantinos, J S Whelan

Journal: Ann. Oncol.. 2003 Feb;14(2):181-90.

 

Despite the use of surgery and radiotherapy, 20-35% of patients with aggressive fibromatosis (AF) will have local recurrence. The purpose of this review was to collect and analyze all available information regarding the role of non-cytotoxic and cytotoxic chemotherapy in AF that has ...

Last Updated: 3 Feb 2003

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Symptoms, Diagnosis, and Treatment

There are currently no related results available in GeneReviews.

There are currently no related results available in Genetic Testing Registry.

 
 
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Clinical Trial Information This information is provided by ClinicalTrials.gov

18F-FES PET/CT in Imaging Patients With Desmoid Tumors
 

Status: Recruiting

Condition Summary: Deep Fibromatosis/Desmoid Tumor; Familial Adenomatous Polyposis

 

Last Updated: 2 Apr 2015

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Sorafenib Tosylate in Treating Patients With Desmoid Tumors or Aggressive Fibromatosis
 

Status: Recruiting

Condition Summary: Desmoid-Type Fibromatosis

 

Last Updated: 24 Aug 2015

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Last Updated: 15 Apr 2015

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