Aggressive Fibromatosis

Common Name(s)

Aggressive Fibromatosis

Description for this condition is not yet available.
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Aggressive Fibromatosis" for support, advocacy or research.

Logo
The Desmoid Tumor Research Foundation

Dedicated to funding research to find a cure for desmoid tumors

Last Updated: 19 Feb 2013

View Details

 

General Support Organizations

Not finding the support you need? Show General Support Organizations

 
 
Top

How do you compare to others with this condition?

Privately answer questions about your health. Let resources, you select, come to you.

Anonymously share and see how your answers compare with others with this condition while privately providing key pieces of information to medical researchers, disease advocacy groups, and others ONLY YOU select to help speed up cures and better alternatives.

 
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Aggressive Fibromatosis" for support, advocacy or research.

Logo
The Desmoid Tumor Research Foundation

Dedicated to funding research to find a cure for desmoid tumors

http://www.dtrf.org

Last Updated: 19 Feb 2013

View Details

 

General Support Organizations

Not finding the support you need? Show General Support Organizations

 
 
 
 
Top

Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Aggressive Fibromatosis" returned 32 free, full-text research articles on human participants. First 3 results:

Targeting stem cell behavior in desmoid tumors (aggressive fibromatosis) by inhibiting hedgehog signaling.
 

Author(s): Ronak Ghanbari-Azarnier, Shingo Sato, Qingxia Wei, Mushriq Al-Jazrawe, Benjamin A Alman

Journal: Neoplasia. 2013 Jul;15(7):712-9.

 

Desmoid tumor (also called aggressive fibromatosis) is a lesion of mesenchymal origin that can occur as a sporadic tumor or a manifestation of the preneoplastic syndrome, familial adenomatous polyposis caused by a mutation in adenomatous polyposis coli (APC). This tumor type is characterized ...

Last Updated: 1 Jul 2013

Go To URL
Aggressive fibromatosis of the oral cavity.
 

Author(s): Santhosh Rao, B S Dinesh

Journal: Indian J Dent Res. ;23(3):435.

 

Fibromatosis are proliferations of highly differentiated fibrous tissue. The deep or musculoaponeurotic types of fibromatosis are known as desmoid tumors, aggressive fibromatosis, or desmoid-type fibrosarcoma. It is commonly seen as abdominal tumors; the occurrence of these tumors ...

Last Updated: 12 Oct 2012

Go To URL
Recurrence and prognostic factors in patients with aggressive fibromatosis. The role of radical surgery and its limitations.
 

Author(s): Emilio Bertani, Alessandro Testori, Antonio Chiappa, Pasquale Misitano, Roberto Biffi, Giuseppe Viale, Giovanni Mazzarol, Tommaso De Pas, Edoardo Botteri, Gianmarco Contino, Francesco Verrecchia, Barbara Bazolli, Bruno Andreoni

Journal:

 

Surgery is still the standard treatment for aggressive fibromatosis (AF); however, local control remains a significant problem and the impact of R0 surgery on cumulative recurrence (CR) is objective of contradictory reports.

Last Updated: 24 Sep 2012

Go To URL

Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Aggressive Fibromatosis" returned 2 free, full-text review articles on human participants. First 3 results:

Pediatric aggressive fibromatosis: a retrospective analysis of 13 patients and review of literature.
 

Author(s): Saskia Buitendijk, Cees P van de Ven, Ton G Dumans, Jan C den Hollander, Peter J Nowak, Wim J Tissing, Rob Pieters, Marry M van den Heuvel-Eibrink

Journal: Cancer. 2005 Sep;104(5):1090-9.

 

Aggressive fibromatosis (AF) is a soft tissue tumor and is rare in childhood, with high potential for local invasiveness and recurrence. General recommendations for the clinical management of pediatric patients with AF remain undetermined.

Last Updated: 29 Aug 2005

Go To URL
The pharmacological treatment of aggressive fibromatosis: a systematic review.
 

Author(s): J Janinis, M Patriki, L Vini, G Aravantinos, J S Whelan

Journal: Ann. Oncol.. 2003 Feb;14(2):181-90.

 

Despite the use of surgery and radiotherapy, 20-35% of patients with aggressive fibromatosis (AF) will have local recurrence. The purpose of this review was to collect and analyze all available information regarding the role of non-cytotoxic and cytotoxic chemotherapy in AF that has ...

Last Updated: 3 Feb 2003

Go To URL
 
 
Top

Symptoms, Diagnosis, and Treatment

There are currently no related results available in GeneReviews.

There are currently no related results available in Genetic Testing Registry.

 
 
Top

Clinical Trial Information This information is provided by ClinicalTrials.gov

Phase II Trial of the Gamma-Secretase Inhibitor PF-03084014 in Adults With Desmoid Tumors/Aggressive Fibromatosis
 

Status: Recruiting

Condition Summary: Desmoid Tumors; Aggressive Fibromatosis

 

Last Updated: 2 Aug 2014

Go to URL
Sorafenib Tosylate in Treating Patients With Desmoid Tumors or Aggressive Fibromatosis
 

Status: Recruiting

Condition Summary: Desmoid Tumor

 

Last Updated: 19 Aug 2014

Go to URL

Last Updated: 13 Feb 2014

Go to URL