Eisenmenger Syndrome

Common Name(s)

Eisenmenger Syndrome

Eisenmenger syndrome is a rare progressive heart condition caused by a structural error in the heart, typically a "hole in the heart" (ventricular septal defect) present at birth (congenital heart defect). This causes abnormal blood flow in the heart, resulting in high pressure within the pulmonary artery, the main blood vessel that connects the heart to the lungs (pulmonary hypertension).
 

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Eisenmenger Syndrome" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Eisenmenger Syndrome" returned 49 free, full-text research articles on human participants. First 3 results:

Eisenmenger syndrome in an adult patient with a large patent ductus arteriosus.
 

Author(s): Konstantinos Dimopoulos

Journal: Eur Respir Rev. 2013 Dec;22(130):558-64.

 

This is the case of a young female who was seen at our adult congenital heart disease and pulmonary hypertension service (Royal Brompton Hospital, London, UK) at the age of 17 years. She initially presented at the age of 4 years with increasing shortness of breath. At that time, there ...

Last Updated: 2 Dec 2013

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Vaginal delivery in a patient of Eisenmenger syndrome.
 

Author(s): Priyanka Kalra

Journal: Indian J Med Sci. ;66(11-12):289-91.

 

Eisenmenger syndrome consists of a congenital communication between the systemic and pulmonary circulation, with resultant pulmonary arterial hypertension and reversal of flow through the defect. Pregnancy in the setting of pulmonary hypertension and Eisenmenger physiology is associated ...

Last Updated: 30 Jul 2013

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Safe management of cesarean section in a patient of Eisenmenger syndrome.
 

Author(s): Silvia Minicucci, Vincenzo Segala, Claudio Verdecchia, Piero Sismondi, Riccardo Casabona, Fabrizio Sansone

Journal: Ann Card Anaesth. ;15(4):296-8.

 

We report our experience of a 29-year-old female with a complete atrio-ventricular septal defect leading to a single ventricle physiology and Eisenmenger syndrome. The patient successfully underwent spinal anesthesia for cesarean section in the 31 st week of pregnancy. A multidisciplinary ...

Last Updated: 8 Oct 2012

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Eisenmenger Syndrome" returned 4 free, full-text review articles on human participants. First 3 results:

Eisenmenger syndrome: not always inoperable.
 

Author(s): Jing-Bin Huang, Jian Liang, Li-Yan Zhou

Journal: Respir Care. 2012 Sep;57(9):1488-95.

 

Recently, advanced therapies for pulmonary arterial hypertension have become available, and have been effective in reducing pulmonary vascular resistance and symptoms in patients with Eisenmenger syndrome, previously thought to be inoperable. This review summarizes the current knowledge ...

Last Updated: 4 Sep 2012

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Therapeutic methods used in patients with Eisenmenger syndrome.
 

Author(s): Olga Trojnarska, Karolina Plaskota

Journal: Cardiol J. 2009 ;16(6):500-6.

 

Patients with Eisenmenger syndrome form a small percentage of congenital heart disease patients. The rarity of this syndrome, combined with its complex pathophysiology, account for the insufficient understanding of the principles underlying its proper treatment. The main clinical ...

Last Updated: 1 Dec 2009

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Eisenmenger syndrome a clinical perspective in a new therapeutic era of pulmonary arterial hypertension.
 

Author(s): Maurice Beghetti, Nazzareno Galiè

Journal: J. Am. Coll. Cardiol.. 2009 Mar;53(9):733-40.

 

Eisenmenger syndrome (ES), the most advanced form of pulmonary arterial hypertension (PAH) associated with congenital heart disease, is a devastating condition that has a considerable impact on patients' lives. Patients who develop ES typically exhibit 1 or more of a range of cardiac ...

Last Updated: 27 Feb 2009

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Symptoms, Diagnosis, and Treatment

There are currently no related results available in GeneReviews.

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Clinical Trial Information This information is provided by ClinicalTrials.gov

MAESTRO-OL: Macitentan in Eisenmenger Syndrome To Restore Exercise Capacity (Open-Label)
 

Status: Recruiting

Condition Summary: Eisenmenger Syndrome

 

Last Updated: 7 Aug 2014

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MAESTRO (Macitentan in Eisenmenger Syndrome To Restore Exercise Capacity)
 

Status: Recruiting

Condition Summary: Eisenmenger Syndrome

 

Last Updated: 7 Aug 2014

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Eisenmenger Syndrome in the Nordic Countries
 

Status: Recruiting

Condition Summary: Eisenmenger Syndrome

 

Last Updated: 29 Oct 2013

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