Eisenmenger Syndrome

Common Name(s)

Eisenmenger Syndrome

Eisenmenger syndrome is a rare progressive heart condition caused by a structural error in the heart, typically a "hole in the heart" (ventricular septal defect) present at birth (congenital heart defect). This causes abnormal blood flow in the heart, resulting in high pressure within the pulmonary artery, the main blood vessel that connects the heart to the lungs (pulmonary hypertension).
 

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How do you compare to others with this condition?

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Eisenmenger Syndrome" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Eisenmenger Syndrome" returned 60 free, full-text research articles on human participants. First 3 results:

Medical treatment for an adult patient with eisenmenger syndrome. A case report.
 

Author(s): Atsushi Yao

Journal: Int Heart J. 2015 ;56 Suppl():S8-11.

 

Previous studies examining the use of pulmonary arterial hypertension (PAH) drugs in patients with Eisenmenger syndrome (ES) have shown that it may have beneficial effects in some patients with ES; however, experience with additional cases is necessary to confirm its efficacy and ...

Last Updated: 19 Mar 2015

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Update on medical treatment of patients with eisenmenger syndrome.
 

Author(s): Hiroyuki Fukushima

Journal: Int Heart J. 2015 ;56 Suppl():S4-7.

 

Eisenmenger syndrome (ES) is the most advanced form of pulmonary arterial hypertension (PAH) associated with congenital heart defects. ES greatly affects functional capacity, quality of life, and survival of patients. Clinical management of patients with ES has been dramatically changed ...

Last Updated: 19 Mar 2015

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[Management of adult patients with Eisenmenger syndrome].
 

Author(s): Meral Kayıkçıoğlu

Journal: Turk Kardiyol Dern Ars. 2014 Sep;42(6):542-4.

 

Last Updated: 3 Nov 2014

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Eisenmenger Syndrome" returned 4 free, full-text review articles on human participants. First 3 results:

Eisenmenger syndrome: not always inoperable.
 

Author(s): Jing-Bin Huang, Jian Liang, Li-Yan Zhou

Journal: Respir Care. 2012 Sep;57(9):1488-95.

 

Recently, advanced therapies for pulmonary arterial hypertension have become available, and have been effective in reducing pulmonary vascular resistance and symptoms in patients with Eisenmenger syndrome, previously thought to be inoperable. This review summarizes the current knowledge ...

Last Updated: 4 Sep 2012

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Therapeutic methods used in patients with Eisenmenger syndrome.
 

Author(s): Olga Trojnarska, Karolina Plaskota

Journal: Cardiol J. 2009 ;16(6):500-6.

 

Patients with Eisenmenger syndrome form a small percentage of congenital heart disease patients. The rarity of this syndrome, combined with its complex pathophysiology, account for the insufficient understanding of the principles underlying its proper treatment. The main clinical ...

Last Updated: 1 Dec 2009

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Eisenmenger syndrome a clinical perspective in a new therapeutic era of pulmonary arterial hypertension.
 

Author(s): Maurice Beghetti, Nazzareno Galiè

Journal: J. Am. Coll. Cardiol.. 2009 Mar;53(9):733-40.

 

Eisenmenger syndrome (ES), the most advanced form of pulmonary arterial hypertension (PAH) associated with congenital heart disease, is a devastating condition that has a considerable impact on patients' lives. Patients who develop ES typically exhibit 1 or more of a range of cardiac ...

Last Updated: 27 Feb 2009

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Symptoms, Diagnosis, and Treatment

There are currently no related results available in GeneReviews.

There are currently no related results available in Genetic Testing Registry.

 
 
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Clinical Trial Information This information is provided by ClinicalTrials.gov

MAESTRO (Macitentan in Eisenmenger Syndrome To Restore Exercise Capacity)
 

Status: Recruiting

Condition Summary: Eisenmenger Syndrome

 

Last Updated: 11 May 2015

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MAESTRO-OL: Macitentan in Eisenmenger Syndrome To Restore Exercise Capacity (Open-Label)
 

Status: Recruiting

Condition Summary: Eisenmenger Syndrome

 

Last Updated: 11 May 2015

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Eisenmenger Syndrome in the Nordic Countries
 

Status: Recruiting

Condition Summary: Eisenmenger Syndrome

 

Last Updated: 4 Nov 2014

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