Dextrocardia

Common Name(s)

Dextrocardia

Dextrocardia is a group of rare heart defects present at birth (congenital). The simplest type occurs when the heart is a mirror image of a normal heart and still functions correctly. Usually the other organs of the body are also in mirror image, but again all organs work correctly. Sometimes babies with dextrocardia also have a problem with the fine hair (cilia) found in the nose and air passages (Kartagener syndrome). More commonly, dextrocardia is found with other heart defects including double outlet right ventricle, endocardial cushion defect, pulmonary atresia, single ventricle, transposition of the great vessels, or ventricular septal defects. Heterotaxy may also be present which is when the organs of the baby are not in the right place and do not work properly.

Symptoms depend on the type of dextrocardia and other birth defects present. If the heart is a complete mirror image, no symptoms may be present. If the condition is more complicated, symptoms may include pale or bluish skin, difficulty breathing, yellowing of the skin or eyes (jaundice), fatigue, slow growth and weight gain, and repeated lung and sinus infections. The cause of dextrocardia is unknown but it can run in families.

Tests including CT scans, electrocardiogram (EKG), cardiac MRI, echocardiogram (ultrasound of heart) and X-rays can confirm the diagnosis and look for other birth defects. A complete mirror image dextrocardia with no other heart defects will not need treatment. If other defects are present, treatment options, including different types of medications and surgery, will depend on the type and severity of the other defects. Research is ongoing so talk to your baby’s heart doctor and other specialist(s) about the most current treatment options. A genetic counselor and support organizations are good sources of information and can help connect you with other families affected by dextrocardia.

Source: Advocacy organizations associated with the condition.

 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Dextrocardia" for support, advocacy or research.

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How do you compare to others with this condition?

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Dextrocardia" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Dextrocardia" returned 98 free, full-text research articles on human participants. First 3 results:

Implantation of VVI pacemaker in a patient with dextrocardia, persistent left superior vena cava, and sick sinus syndrome: A case report.
 

Author(s): Gongliang Guo, Lili Yang, Jinyi Wu, Liqun Sun

Journal: Medicine (Baltimore). 2017 Feb;96(5):e6028.

 

Dextrocardia, or right-lying heart, is an uncommon congenital heart disease in which the apex of the heart is located on the right side of chest. Persistent left superior vena cava (PLSVA) is a rare venous anomaly that is often associated with the abnormalities of cardiac transduction ...

Last Updated: 2 Feb 2017

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Criss-cross heart with dextrocardia and transposition of the great arteries: a rare pathology.
 

Author(s): Taner Kasar, Pelin Ayyıldız, Aysel Türkvatan, Yakup Ergül, Alper Güzeltaş

Journal: Turk Kardiyol Dern Ars. 2016 Jan;44(1):91.

 

Last Updated: 15 Feb 2016

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Fontan's circulation with dextrocardia, recent pulmonary embolism, and inferior vena cava filter: Anesthetic challenges for urgent hysterectomy.
 

Author(s): Preet Mohinder Singh, Anuradha Borle, Rashmi Ramachandran, Anjan Trikha, Basavana Gouda Goudra

Journal: Ann Card Anaesth. ;19(1):177-81.

 

Fontan's circulation is a unique challenge for the anesthesiologist. Venous pressure is the only source of blood flow for the pulmonary circulation. Patients with such circulation are extremely sensitive to progression of cyanosis (decreased pulmonary blood flow) or circulatory failure. ...

Last Updated: 11 Jan 2016

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Dextrocardia" returned 4 free, full-text review articles on human participants. First 3 results:

Tetralogy of fallot with dextrocardia and situs inversus in a 7-year-old boy.
 

Author(s): Michael Dilorenzo, Samuel Weinstein, Rajesh Shenoy

Journal: Tex Heart Inst J. 2013 ;40(4):481-3.

 

Tetralogy of Fallot is one of the most frequently diagnosed congenital cardiac abnormalities; however, its association with dextrocardia and situs inversus is reported only rarely. We report a case of these findings in a 7-year-old boy, describe the patient's postoperative course, ...

Last Updated: 1 Oct 2013

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Endovascular repair of blunt aortic injury in a patient with situs inversus and dextrocardia.
 

Author(s): John F Bilello, Peter L Birnbaum, Chandra Venugopal, Leo L Fong

Journal: J. Vasc. Surg.. 2011 Sep;54(3):857-9.

 

A 24-year-old male pedestrian with situs inversus and dextrocardia was struck by a car and sustained multiple injuries, including a pseudoaneurysm of the proximal descending thoracic aorta. A thoracic endograft was deployed to exclude the blunt aortic injury. We are not aware of any ...

Last Updated: 5 Sep 2011

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Primary angioplasty and later elective multivessel stenting in a patient with dextrocardia: a case report and literature review.
 

Author(s): Elbagir Elbasheer, Abdelhakim Habib, Adil Salam

Journal: J Invasive Cardiol. 2010 Jul;22(7):E125-8.

 

Dextrocardia is a rare congenital anomaly with a prevalence of 1 in 10,000 births. The incidence of coronary artery disease in such patients is thought to be similar to that of the general public, however, patients are seldom seen during routine clinical practice and at the cardiac ...

Last Updated: 6 Jul 2010

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Symptoms, Diagnosis, and Treatment

There are currently no related results available in GeneReviews.

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Clinical Trial Information This information is provided by ClinicalTrials.gov

Transcatheter Valve Implantation in Patients With Dysfunctional Left and Right Sided Heart Valves
 

Status: Recruiting

Condition Summary: Eisenmenger Syndrome

 

Last Updated: 3 Jun 2016

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Ambrisentan in Single Ventricle
 

Status: Recruiting

Condition Summary: Hypoplastic Left Heart Syndrome; Hypoplastic Right-sided Heart Complex

 

Last Updated: 17 Aug 2016

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Open Lung Strategy in Critically Ill Morbid Obese Patients
 

Status: Recruiting

Condition Summary: Obesity; Respiratory Insufficiency; Right-Sided Heart Failure; Pulmonary Atelectasis; Respiratory Mechanics

 

Last Updated: 8 Feb 2017

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