Dermatofibrosarcoma protuberans

Common Name(s)

Dermatofibrosarcoma protuberans

Dermatofibrosarcoma protuberans is an uncommon tumor that arises in the skin. The tumor is firm and often flesh-colored although it can be reddish, bluish, or purplish. The tumor is often found on the chest or shoulders, but it can be found on other parts of the body. Dermatofibrosarcoma protuberans may cause no symptoms, and the initial size of the tumor tends to be around 1 to 5 centimeters. This tumor has a low potential to spread to other tissues. Treatment often involves surgery to remove the tumor, such as by Mohs’ micrographic surgery. If you or a family member has been diagnosed with dermatofibrosarcoma protuberans, talk with your doctor about the most current treatment options.
 

Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Dermatofibrosarcoma protuberans" for support, advocacy or research.

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Sarcoma Alliance

The Sarcoma Alliance strives to improve the lives of people affected by sarcoma through accurate diagnosis, improved access to care, guidance, education and support.

Last Updated: 20 Feb 2013

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How do you compare to others with this condition?

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Dermatofibrosarcoma protuberans" for support, advocacy or research.

Logo
Sarcoma Alliance

The Sarcoma Alliance strives to improve the lives of people affected by sarcoma through accurate diagnosis, improved access to care, guidance, education and support.

http://sarcomaalliance.org

Last Updated: 20 Feb 2013

View Details

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Dermatofibrosarcoma protuberans" returned 95 free, full-text research articles on human participants. First 3 results:

Breast and pleuropulmonary metastasis of multirecurrent scalp dermatofibrosarcoma protuberans: a case report.
 

Author(s): N-A Ouédraogo Nde, N A Ouédraogo, H A Bambara, B M A Tiemtoré-Kambou, F Traoré, N Zongo, M S Ouédraogo, G P Tapsoba, Achach Thouraya Chtioui, A Lamien/Sanou

Journal:

 

Dermatofibrosarcoma protuberans is a rare tumor, representing about 0.1% of skin malignant tumors. It is characterized by local aggressiveness with significant potential for recurrence. Although metastasis is rare, it does occur. We report a case of a Burkinabe woman with dermatofibrosarcoma ...

Last Updated: 8 Apr 2017

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A single-institutional review of 68 patients with dermatofibrosarcoma protuberans: wide re-excision after inadequate previous surgery results in a high rate of local control.
 

Author(s): Kamran Harati, Kim Lange, Ole Goertz, Armin Lahmer, Nicolai Kapalschinski, Ingo Stricker, Marcus Lehnhardt, Adrien Daigeler

Journal:

 

Dermatofibrosarcoma protuberans (DFSP) is a cutaneous soft tissue sarcoma characterized by an indolent but aggressive local growth. Unplanned excisions with positive margins are common, and the prognostic impact of radical re-excisions is still unclear. The aim of the present study ...

Last Updated: 6 Jan 2017

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Dermatofibrosarcoma Protuberans-Like Tumor With COL1A1 Copy Number Gain in the Absence of t(17;22).
 

Author(s): Jad Saab, Ian M Rosenthal, Lu Wang, Klaus J Busam, Kishwer S Nehal, Mark A Dickson, Meera R Hameed, Travis J Hollmann

Journal: Am J Dermatopathol. 2017 Apr;39(4):304-309.

 

A 57-year-old woman presented with a 3-year history of a progressive firm plaque on the right cheek. Skin biopsies revealed a bland, storiform, spindle-cell proliferation involving the deep dermis and subcutaneous fat. By immunohistochemistry, the tumor cells were diffusely positive ...

Last Updated: 16 Dec 2016

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Dermatofibrosarcoma protuberans" returned 10 free, full-text review articles on human participants. First 3 results:

18F-FDG PET/CT Prediction of an Aggressive Clinical Course for Dermatofibrosarcoma Protuberans.
 

Author(s): Sandip Basu, Fahim Goliwale

Journal: J Nucl Med Technol. 2016 Jun;44(2):88-9.

 

The ability to assess tumor biology is a benefit of molecular imaging with (18)F-FDG PET/CT, which performs better than anatomic imaging in evaluating malignancies. We present an unusual case of fatal dermatofibrosarcoma protuberans, a usually indolent entity for which high-grade ...

Last Updated: 4 Jun 2016

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Unusual presentation of dermatofibrosarcoma protuberans in a male patient's breast: a case report and review of the literature.
 

Author(s): Mohannad Al Tarakji, Adriana Toro, Isidoro Di Carlo, Kulsoon Junejo

Journal:

 

We herein present a case report and literature review of dermatofibrosarcoma protuberans in the breast of a male patient. A 27-year-old man presented with a painless lump in his right breast with areas of bluish skin discoloration. The diagnostic work-up comprised clinical examination, ...

Last Updated: 3 Aug 2015

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[Dermatofibrosarcoma protuberans : report of 27 cases and review of the literature].
 

Author(s): Nawal Hammas, Ikram Badioui, Kaoutar Znati, Amal Benlemlih, Laila Chbani, Hind El Fatemi, Taoufiq Harmouch, Youssef Bouyahyaoui, Faouzi Boutayeb, Abdelmajid Mrini, Omar Mesbahi, Fatima Zahra Mernissi, Afaf Amarti

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Last Updated: 9 Dec 2014

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Clinical Trial Information This information is provided by ClinicalTrials.gov

Spanish Registry of Mohs Surgery
 

Status: Recruiting

Condition Summary: Skin Neoplasms; Carcinoma, Basal Cell; Carcinoma, Squamous Cell; Dermatofibrosarcoma; Melanoma; Histiocytoma, Malignant Fibrous; Neoplasms, Adnexal and Skin Appendage

 

Last Updated: 11 Sep 2016

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To Find a Safe Dose and Show Early Clinical Activity of Weekly Nab-paclitaxel in Pediatric Patients With Recurrent/ Refractory Solid Tumors
 

Status: Recruiting

Condition Summary: Neuroblastoma; Rhabdomyosarcoma; Ewing's Sarcoma; Ewing's Tumor; Sarcoma, Ewing's; Sarcomas, Epitheliod; Sarcoma, Soft Tissue; Sarcoma, Spindle Cell; Melanoma; Malignant Melanoma; Clinical Oncology; Oncology, Medical; Pediatrics, Osteosarcoma; Osteogenic Sarcoma; Osteosarcoma Tumor; Sarcoma, Osteogenic; Tumors; Cancer; Neoplasia; Neoplasm; Histiocytoma; Fibrosarcoma; Dermatofibrosarcoma

 

Last Updated: 29 Aug 2017

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