Congenital Hepatic Fibrosis

Common Name(s)

Congenital Hepatic Fibrosis

Description for this condition is not yet available.
 

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Advocacy and Support Organizations

 

Condition Specific Organizations

Following organizations serve the condition "Congenital Hepatic Fibrosis" for support, advocacy or research.

There are currently no organizations listed in Disease InfoSearch that support this condition. Create a listing.

 

 

General Support Organizations

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Scientific Literature

Articles from the PubMed Database

Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Congenital Hepatic Fibrosis" returned 39 free, full-text research articles on human participants. First 3 results:

Laparoscopic distal splenoadrenal shunt for the treatment of portal hypertension in children with congenital hepatic fibrosis: A case report.
 

Author(s): Jin-Shan Zhang, Wei Cheng, Long Li

Journal: Medicine (Baltimore). 2017 Jan;96(3):e5843.

 

The distal splenorenal shunt is an effective procedure for the treatment of portal hypertension in children. However, there has been no report about laparoscopic distal splenorenal shunt in the treatment of portal hypertension in children.

Last Updated: 18 Jan 2017

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Pediatric living donor liver transplantation for congenital hepatic fibrosis using a mother's graft with von Meyenburg complex: A case report.
 

Author(s): Naoya Yamada, Yukihiro Sanada, Takumi Katano, Masahisa Tashiro, Yuta Hirata, Noriki Okada, Yoshiyuki Ihara, Atsushi Miki, Hideki Sasanuma, Taizen Urahashi, Yasunaru Sakuma, Koichi Mizuta

Journal: World J. Gastroenterol.. 2016 Nov;22(44):9865-9870.

 

This is the first report of living donor liver transplantation (LDLT) for congenital hepatic fibrosis (CHF) using a mother's graft with von Meyenburg complex. A 6-year-old girl with CHF, who suffered from recurrent gastrointestinal bleeding, was referred to our hospital for liver ...

Last Updated: 13 Dec 2016

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Congenital hepatic fibrosis: clinical presentation, laboratory features and management at a tertiary care hospital of Lahore.
 

Author(s): Arit Parkash, Huma Arshad Cheema, Hassan Suleman Malik, Zafar Fayyaz

Journal: J Pak Med Assoc. 2016 Aug;66(8):984-8.

 

To describe the clinical presentations, laboratory features and management of congenital hepatic fibrosis patients at a tertiary care hospital.

Last Updated: 15 Aug 2016

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Reviews from the PubMed Database

Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Congenital Hepatic Fibrosis" returned 6 free, full-text review articles on human participants. First 3 results:

Evidence for a "Pathogenic Triumvirate" in Congenital Hepatic Fibrosis in Autosomal Recessive Polycystic Kidney Disease.
 

Author(s): Lu Jiang, Pingping Fang, James L Weemhoff, Udayan Apte, Michele T Pritchard

Journal: Biomed Res Int. 2016 ;2016():4918798.

 

Autosomal recessive polycystic kidney disease (ARPKD) is a severe monogenic disorder that occurs due to mutations in the PKHD1 gene. Congenital hepatic fibrosis (CHF) associated with ARPKD is characterized by the presence of hepatic cysts derived from dilated bile ducts and a robust, ...

Last Updated: 28 Nov 2016

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Congenital hepatic fibrosis in autosomal recessive polycystic kidney disease.
 

Author(s): Jessica Wen

Journal: Clin Transl Sci. 2011 Dec;4(6):460-5.

 

Autosomal recessive polycystic kidney disease (ARPKD) is a developmental disorder that mainly affects the kidneys and the biliary tract. Affected patients often have massively enlarged cystic kidneys as well as congenital hepatic fibrosis (CHF) characterized by dilated bile ducts ...

Last Updated: 3 Jan 2012

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Congenital hepatic fibrosis and autosomal recessive polycystic kidney disease.
 

Author(s): Arvind Srinath, Benjamin L Shneider

Journal: J. Pediatr. Gastroenterol. Nutr.. 2012 May;54(5):580-7.

 

The published natural history of congenital hepatic fibrosis (CHF) was examined to inform clinical decision making in autosomal recessive polycystic kidney disease (ARPKD).

Last Updated: 13 Apr 2012

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Clinical Trial Information This information is provided by ClinicalTrials.gov

Natural History of Noncirrhotic Portal Hypertension
 

Status: Recruiting

Condition Summary: Cystic Fibrosis; Immunologic Deficiency Syndrome; Turner Syndrome; Congenital Hepatic Fibrosis; Idiopathic Non-Cirrhotic Portal Hypertension

 

Last Updated: 30 Jun 2017

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UAB HRFD Core Center: Core A: The Hepato/Renal Fibrocystic Diseases Translational Resource
 

Status: Recruiting

Condition Summary: Hepato/Renal Fibrocystic Disease; Autosomal Recessive Polycystic Kidney Disease; Joubert Syndrome; Bardet Biedl Syndrome; Meckel-Gruber Syndrome; Congenital Hepatic Fibrosis; Caroli Syndrome; Oro-Facial-Digital Syndrome Type I; Nephronophthisis; Glomerulocystic Kidney Disease

 

Last Updated: 23 Aug 2016

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Clinical and Molecular Investigations Into Ciliopathies
 

Status: Recruiting

Condition Summary: Autosomal Recessive Polycystic Kidney Disease; Congenital Hepatic Fibrosis; Caroli's Disease; Polycystic Kidney Disease; Joubert Syndrome; Cerebro-Oculo-Renal Syndromes; COACH Syndrome; Senior-Loken Syndrome; Dekaban-Arima Syndrome; Cogan Oculomotor Apraxia; Nephronophthisis; Bardet-Biedl Syndrome; Alstrom Syndrome; Oral-Facial-Digital Syndrome

 

Last Updated: 1 Jul 2017

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